Sapporo Medical Journal

Abstract : The aim of this study is to evaluate the frequency of patients with anorectal anomalies (ARA) associated with CHD at a tertiary care hospital in a 5 years period. Methods: This retrospective study reviewed the filling system of all children who underwent surgical correction for ARA either of high or low type in a 5 years period from January 2012 until December 2017. Various assessment measures were evaluated and reported including; clinical examination, electrocardiography (ECG), chest radiography, and color Doppler echocardiography. Results: Sixty-three patients with ARA were studied. They were 44 males and 19 females with a male to female ratio of (2.3: 1). Out of the total patients, 41 showed CHD with a percentage of 65.1%. CHD types varied from atrial-septal defect (ASD) in 28 patients (68.3%), coarctation of the aorta in 2 patients (4.9%), mixed anomalies of ASD associated with ventricular-septal defect (VSD) and patent ductus arteriosus (PDA) in 8 patients (19.5%). Two patients (4.9%) showed multiple CHD that were ASD + PDA while the remaining one (2.4%) were having VSD. Conclusion: The frequency of CHD in patients with ARA was very high. The commonest CHD encountered presentation was ASD. The current reported data indicate the needs to establish larger scale studies at national or international levels for accurately determine the frequency of CHD in ARA patients.